Congenital mesoblastic nephroma: A case report and review of literature

Authors

  • Bwala KJ Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Umar AM Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Suleiman DE Histopathology Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Abdullahi I Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Zaidu am Paediatric Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Mustapha SS Paediatric Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Adamu D Histopathology Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Habibu KA Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Aliyu NS Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi
  • Alhassan N Surgery Department, Abubakar Tafawa Balewa University Teaching Hospital, ATBUTH, Bauchi

DOI:

https://doi.org/10.61386/imj.v18i3.718

Keywords:

congenital, mesoblastic nephroma, emergency surgery

Abstract

Introduction: Congenital mesoblastic nephroma is a rare renal tumour affecting newborns and infants. It is also known as leiomyomatous or fetal hamartoma and is the most common solid Renal tumor in the neonate and infants less than 6 months old.

Case summary: We report a case of congenital mesoblastic nephroma (CMN) in a 19-hour-old boy presenting with a huge intra-abdominal mass and failure to pass meconium. Ultrasound scan revealed a huge intra-abdominal mass arising from the left renal bed and gaseous intestinal dilatation. Emergency simple total left nephrectomy was done, and histological diagnosis of CMN was confirmed. The newborn was discharged in good condition 5 days after surgery.

Conclusion: A high index of suspicion and prompt surgical intervention are crucial for a favourable outcome.

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Published

01-07-2025